Dyke-Davidoff-Masson syndrome is characterized by unilateral atrophy of cerebral hemispheres, enlargement of the ipsilateral sulci, ventricles, and cisternal sp. Dyke-Davidoff-Masson syndrome is a rare condition of unknown frequency resulting from brain injury due to a multitude of causes; especially in. Dyke-Davidoff-Masson Syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere. (hemiatrophy) which is secondary to brain insult.
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Introduction Dyke—Davidoff—Masson syndrome DDMS is described as skull radiographic and pneumatoencephalographic changes in daviroff series of nine patients whose clinical characteristics included hemiparesis, seizures, facial asymmetry, and mental retardation which was proposed in by Dyke et al.
Koshy B, Surendrababu NR.
There was no history of significant antenatal or perinatal complications. These clinical and radiological findings are suggestive of DDMS.
He responded well to the drug followed by sessions of physiotherapy. It usually presents with intractable focal epilepsy and cognitive defects in children.
Birth trauma, hypoxia, intracranial hemorrhage, tumors, infections, and prolonged febrile seizures after birth are important peri- and post-natal causes.
Elevation of the petrous ridge and ipsilateral falcine displacement may also be present. There was subtle thickening of the left hemicranium noted, measuring 4. About Blog Go ad-free. Sign in to customize your interests Sign in to your personal account.
Development of the Nervous system. J Neurosci Rural Pract. Magnetic resonance imaging of the brain showing diffuse atrophy of the left cerebral hemisphere with dilatation of the left lateral ventricle and prominence masaon sulci over the left cerebral hemisphere. Cerebral hemiatrophy, Dyke—Davidoff—Masson syndrome, hemiparesis.
Ind J Radiol Imag. Seizures, facial asymmetry, contralateral hemiplegia or hemiparesis, mental retardation, and rarely, patients can also present with sensory symptoms and psychiatric disorders such as schizophrenia.
National Center for Biotechnology InformationU. Coarctation of midaortic arch presenting with monoparesis.
Important differential diagnosis includes — Sturge—Weber Syndrome, basal cell germinoma, Fishman davidofff, Silver—Russell syndrome, linear nevus syndrome, and Rasmussen encephalitis. Sensory loss and amsson manifestations like schizophrenia had been reported rarely.
When DDMS develops early in life during the first 2 yearscertain cranial changes such as ipsilateral hypertrophy of the skull and enlargement of sinuses occur, the elevations of the greater wing of sphenoid and the petrous ridge on the affected side and ipsilateral falcine displacement.
The convulsion was followed by decreased movement of the right side of the body and drooling of saliva from the right side occasionally, for which the patient was given some native medication. Internet J Pediatr Neonatol. Dyke—Davidoff—Masson syndrome DDMS is described as skull radiographic and pneumatoencephalographic changes in their series of nine patients whose clinical characteristics included hemiparesis, seizures, facial asymmetry, and mental retardation which was proposed in by Dyke et al.
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There are two types of DDMS — congenital infantile and acquired. Abstract Dyke—Davidoff—Masson syndrome DDMS is an uncommon condition, in which the diagnosis is mainly done by jasson clinical presentations along with positive radiological findings. Sign in to make a comment Sign in to your personal account. Footnotes Source of Support: Clinical presentations include variable degree of facial asymmetry, seizures, contralateral hemiparesis, mental retardation, learning disabilities, impaired speech, etc.
Age of presentation depends on time of insult and characteristic changes may be seen only in adolescence or adult. Sign in to download free article PDFs Sign in to access your subscriptions Mxsson in to your personal account. In some sources, it is equated to hemispheric infarctionwhereas in other sources any cause of cerebral hemiatrophy is included.
Sign in to access your subscriptions Sign in to your personal account. By the end of the eighth month, all the important sulci can be recognized. Case 3 Case 3.
Case 5 Case 5. The patient did not attend school. Patients have facial asymmetry, seizures, learning difficulties, and contralateral hemiparesis. A davivoff history, thorough clinical examination, and radiologic findings provide the correct diagnosis.
There was no history of head trauma. This syndrome is usually seen during adolescence; however, it can also be seen in childhood. There was also mild atrophy of the left cerebral peduncle. Author information Copyright and License information Disclaimer. massson
Dyke–Davidoff–Masson syndrome: A rare cause of cerebral hemiatrophy in children
In the patient mentioned above, single episode of seizure was trailed by hemiparesis and mental deterioration. Introduction Dyke-Davidoff-Masson syndrome DDMS refers to atrophy or hypoplasia of one cerebral hemisphere hemiatrophywhich is usually due to an insult to the developing brain in fetal or early childhood period.
Get free access to newly published articles Create a personal account or sign in to: Dyke-Davidoff-Masson syndrome DDMS refers to atrophy or hypoplasia of one cerebral hemisphere hemiatrophywhich is usually due to an insult to the developing brain in fetal or early childhood period.
Thank you for updating your details. He was seizure free for next 3 months but then unfortunately lost for follow-up. The patient may present with seizure and cerebral imaging may show calcified cortex and hemiatrophy.